A Rare Presentation of Os Odontoideum with Multiple Vertebral Fusion in Type III Klippel-Feil Syndrome (KFS) - A Case Report.
نویسندگان
چکیده
An abnormal atlas and axis with presence of os odontoideum and fusion of multiple vertebrae were noted in an intact skeleton, in the osteology museum of the Department of Anatomy of North Bengal Medical College, West Bengal, India.These multiple abnormalities at various levels along with increased thickness of antero-posterior arch of atlas pointed towards the congenital nature of the anomalies, possibly due to Klippel-Feil syndrome (KFS). These unusual findings denote a developmental background of the manifestations.The cervical instability, resultant neurodeficit and impairment of quality of life of the affected individuals, which are inherent in such cases, reveal their clinical importance.
منابع مشابه
Klippel-Feil syndrome: a case report.
OBJECTIVE To report the clinical presentation and peculiarity of management of Klippel-Feil syndrome (KFS) at the University of Abuja Teaching Hospital, Gwagwalada. BACKGROUND KFS is a rare pathology that has not been previously reported on in Nigeria. METHODS Case review was employed to report this pathology. RESULT This case is a 10 year old boy with KFS presenting with cosmetic blemish...
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Patients with Klippel-Feil Syndrome (KFS) have congenital fusion of their cervical vertebrae due to a failure in the normal segmentation of the cervical vertebrae during the early weeks of gestation and also have myriad of other associated anomalies. Because of limited neck mobility, airway management in these patients can be a challenge for the anesthesiologist. We describe a unique case in wh...
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Klippel-Feil Syndrome (KFS) is a complex, congenital condition, originally described by Maurice Klippel and Andre Feil in 1912.1 It is characterized by congenital fusion of two or more cervical vertebrae. Because of the abnormal fusion process and altered spinal biomechanics with undue motion at the non-fused cervical segment, adjacent to fused segments, such individuals are predisposed to abno...
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ورودعنوان ژورنال:
- Journal of clinical and diagnostic research : JCDR
دوره 8 9 شماره
صفحات -
تاریخ انتشار 2014